{"id":7921,"date":"2024-02-05T06:35:00","date_gmt":"2024-02-05T09:35:00","guid":{"rendered":"https:\/\/gastropedia.pub\/pt\/?p=7921"},"modified":"2024-02-13T09:52:28","modified_gmt":"2024-02-13T12:52:28","slug":"neoplasia-pseudopapilar-solida-do-pancreas-tumor-de-frantz","status":"publish","type":"post","link":"https:\/\/gastropedia.pub\/pt\/cirurgia\/hepatopancreatobiliar\/neoplasia-pseudopapilar-solida-do-pancreas-tumor-de-frantz\/","title":{"rendered":"Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (Tumor de Frantz)"},"content":{"rendered":"<div class=\"pdfprnt-buttons pdfprnt-buttons-post pdfprnt-top-right\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/7921?print=pdf\" class=\"pdfprnt-button pdfprnt-button-pdf\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/pdf.png\" alt=\"image_pdf\" title=\"Ver PDF\" \/><\/a><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/7921?print=print\" class=\"pdfprnt-button pdfprnt-button-print\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/print.png\" alt=\"image_print\" title=\"Conte\u00fado de impress\u00e3o\" \/><\/a><\/div>\n<p>A Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (NPSP), conhecida previamente como Tumor de Frantz, \u00e9 um tumor geralmente benigno, por\u00e9m com potencial de malignidade. Estas les\u00f5es s\u00e3o raras, representando menos de 2% das neoplasias pancre\u00e1ticas. Predominam em mulheres jovens (20-30 anos), sendo geralmente assintom\u00e1ticas. Quando h\u00e1 sintomas, o principal deles \u00e9 a dor abdominal. Geralmente s\u00e3o encontrados de forma incidental em exames de imagem como tomografia computadorizada e resson\u00e2ncia magn\u00e9tica. Nesse artigo, vamos resumir as principais caracter\u00edsticas desta neoplasia.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-apresentacao-clinica\"><strong>Apresenta\u00e7\u00e3o Cl\u00ednica:<\/strong><\/h2>\n\n\n\n<p>No passado, a maioria dos casos desta neoplasia eram sintom\u00e1ticos (80%). No entanto, com a utiliza\u00e7\u00e3o disseminada dos m\u00e9todos de imagem, houve grande aumento dos achados incidentais em pacientes assintom\u00e1ticos, que atualmente representam cerca de 50% dos casos. O sintoma mais comum \u00e9 dor abdominal, seguido de n\u00e1useas, v\u00f4mitos e perda de peso. Outros sintomas menos frequentes incluem icter\u00edcia e pancreatite. Alguns pacientes podem apresentar massa palp\u00e1vel, visto que a les\u00e3o n\u00e3o costuma causar sintomas nos est\u00e1gios iniciais.<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Representam menos de 2% das neoplasias pancre\u00e1ticas.<\/li>\n\n\n\n<li>Predominantes em mulheres jovens (20-30 anos).<\/li>\n\n\n\n<li>Geralmente s\u00e3o assintom\u00e1ticos.<\/li>\n\n\n\n<li>Principal sintoma: dor abdominal.<\/li>\n\n\n\n<li>Diagn\u00f3sticos incidentais em TC, RM e US.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-caracteristicas-nos-exames-de-imagem\"><strong>Caracter\u00edsticas nos exames de imagem:<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>As NPSP podem aparecer como uma les\u00e3o pancre\u00e1tica mista, s\u00f3lida e c\u00edstica, em imagens de TC e RNM.<\/li>\n\n\n\n<li>Tamb\u00e9m podem aparecer como tumores s\u00f3lidos bem demarcados.<\/li>\n\n\n\n<li>Num estudo das caracter\u00edsticas de RM de pequenos tumores s\u00f3lidos do p\u00e2ncreas, os NPSP apresentavam uma intensidade de sinal significativamente mais baixa nas imagens ponderadas em T1, uma intensidade de sinal mais elevada nas imagens ponderadas em T2 e um realce heterog\u00eaneo e progressivo precoce na RM, em compara\u00e7\u00e3o com os adenocarcinomas e os tumores neuroend\u00f3crinos.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-caracteristicas-endoscopicas-eus\"><strong>Caracter\u00edsticas Endosc\u00f3picas (EUS):<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Les\u00f5es geralmente s\u00e3o bem demarcadas (aspecto encapsulado), hipoecog\u00eanicas e de apar\u00eancia s\u00f3lida.<\/li>\n\n\n\n<li>Podem ter \u00e1reas c\u00edsticas de permeio, proporcionando uma imagem heterog\u00eanea, ou ser predominantemente c\u00edsticas.<\/li>\n\n\n\n<li>Podem ser encontradas em qualquer lugar do p\u00e2ncreas: cabe\u00e7a, corpo, cauda e processo uncinado.<\/li>\n\n\n\n<li>Calcifica\u00e7\u00f5es podem estar presentes em at\u00e9 20% dos casos.<\/li>\n\n\n\n<li>Outra caracter\u00edstica que pode ser encontrada \u00e9 a presen\u00e7a de vasos no interior do tumor, que podem ser vis\u00edveis como pequenas estruturas hiperecog\u00eanicas que atravessam a les\u00e3o.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-diagnostico-por-eus-fna\"><strong>Diagn\u00f3stico por EUS-FNA:<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>O fluido aspirado do cisto \u00e9 tipicamente sanguinolento.<\/li>\n\n\n\n<li>Sensibilidade: 80-90%, Especificidade: 85-96%.<\/li>\n\n\n\n<li>Fornece informa\u00e7\u00f5es morfol\u00f3gicas para planejamento cir\u00fargico.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-caracteristicas-histologicas-e-marcadores-moleculares\"><strong>Caracter\u00edsticas Histol\u00f3gicas e Marcadores Moleculares:<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>A citologia \u00e9 diagn\u00f3stica em 75% dos casos.<\/li>\n\n\n\n<li>Apresentam estrutura complexa de c\u00e9lulas poligonais.<\/li>\n\n\n\n<li>A disposi\u00e7\u00e3o das c\u00e9lulas tumorais ao redor dos vasos capilares confere \u00e0 les\u00e3o uma apar\u00eancia &#8220;pseudopapilar&#8221; irregular.<\/li>\n\n\n\n<li>A an\u00e1lise citol\u00f3gica revela papilas ramificadas caracter\u00edsticas com estroma mixoide.<\/li>\n\n\n\n<li>A an\u00e1lise imuno-histoqu\u00edmica, incluindo vimentina, CD10 e beta-catenina, auxilia a diferencia\u00e7\u00e3o entre uma NPSP e um tumor neuroend\u00f3crino pancre\u00e1tico.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-caracteristicas-sugestivas-de-malignidade\"><strong>Caracter\u00edsticas Sugestivas de Malignidade:<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Tamanho &gt; 5 cm.<\/li>\n\n\n\n<li>Mitoses frequentes.<\/li>\n\n\n\n<li>\u00cdndice Ki-67 elevado (&gt; 5%).<\/li>\n\n\n\n<li>Invas\u00e3o vascular ou linf\u00e1tica.<\/li>\n\n\n\n<li>Presen\u00e7a de necrose.<\/li>\n\n\n\n<li>Presen\u00e7a de met\u00e1stases \u00e0 dist\u00e2ncia.<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-tratamento-e-prognostico\"><strong>Tratamento e Progn\u00f3stico:<\/strong><\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Ressec\u00e7\u00e3o cir\u00fargica completa \u00e9 a abordagem definitiva, devido ao potencial de maligniza\u00e7\u00e3o.<\/li>\n\n\n\n<li>Escolha cir\u00fargica \u00e9 baseada na localiza\u00e7\u00e3o (duodenopancreatectomia ou pancreatectomia distal).<\/li>\n\n\n\n<li>Sobrevida p\u00f3s-operat\u00f3ria pr\u00f3xima de 95%, com necessidade de monitoramento.<\/li>\n\n\n\n<li>Acompanhamento a longo prazo \u00e9 essencial para identificar recorr\u00eancias.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-gallery has-nested-images columns-default is-cropped wp-block-gallery-1 is-layout-flex wp-block-gallery-is-layout-flex\">\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-01-LESAO-ISOECOICA.jpg\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" width=\"473\" height=\"341\" data-id=\"7922\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-01-LESAO-ISOECOICA.jpg\" alt=\"\" class=\"wp-image-7922\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-01-LESAO-ISOECOICA.jpg?v=1706709522 473w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-01-LESAO-ISOECOICA-300x216.jpg?v=1706709522 300w\" sizes=\"(max-width: 473px) 100vw, 473px\" \/><\/a><figcaption class=\"wp-element-caption\">Paciente de 37 anos, do sexo feminino, com dor abdominal. Observa-se les\u00e3o isoecoica, de aspecto s\u00f3lido e encapsulado, com \u00e1reas c\u00edsticas de permeio, sem calcifica\u00e7\u00f5es e com fluxo pobre ao Doppler, localizada em cabe\u00e7a de p\u00e2ncreas.<\/figcaption><\/figure>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-02-Elastografia-da-lesao.jpg\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" width=\"421\" height=\"311\" data-id=\"7923\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-02-Elastografia-da-lesao.jpg\" alt=\"\" class=\"wp-image-7923\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-02-Elastografia-da-lesao.jpg?v=1706709812 421w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-02-Elastografia-da-lesao-300x222.jpg?v=1706709812 300w\" sizes=\"(max-width: 421px) 100vw, 421px\" \/><\/a><figcaption class=\"wp-element-caption\">Elastografia da les\u00e3o, mostrando aspecto endurecido (predomin\u00e2ncia de \u00e1reas com colora\u00e7\u00e3o azulada).<\/figcaption><\/figure>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-03-Dimensoes-da-lesao.jpg\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" width=\"426\" height=\"317\" data-id=\"7924\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-03-Dimensoes-da-lesao.jpg\" alt=\"\" class=\"wp-image-7924\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-03-Dimensoes-da-lesao.jpg?v=1706709815 426w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-03-Dimensoes-da-lesao-300x223.jpg?v=1706709815 300w\" sizes=\"(max-width: 426px) 100vw, 426px\" \/><\/a><figcaption class=\"wp-element-caption\">Dimens\u00f5es da les\u00e3o (42,5 x 36,5 mm).<\/figcaption><\/figure>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-04-Puncao-da-lesao.jpg\" data-rel=\"penci-gallery-image-content\" ><img loading=\"lazy\" decoding=\"async\" width=\"424\" height=\"309\" data-id=\"7925\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-04-Puncao-da-lesao.jpg\" alt=\"\" class=\"wp-image-7925\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-04-Puncao-da-lesao.jpg?v=1706709817 424w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2024\/01\/FIGURA-04-Puncao-da-lesao-300x219.jpg?v=1706709817 300w\" sizes=\"(max-width: 424px) 100vw, 424px\" \/><\/a><figcaption class=\"wp-element-caption\">Pun\u00e7\u00e3o da les\u00e3o.<\/figcaption><\/figure>\n<\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-\"><\/h2>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-referencias\"><strong>Refer\u00eancias:<\/strong><\/h2>\n\n\n\n<ol class=\"wp-block-list\">\n<li>Arief Suriawinata.Pathology of exocrine pancreatic neoplasms. Uptodate 2023. Disponivel em: <a href=\"https:\/\/na01.safelinks.protection.outlook.com\/?url=https%3A%2F%2Fwww.uptodate.com%2Fcontents%2Fpathology-of-exocrine-pancreatic-neoplasms%2Fcontributors&amp;data=05%7C01%7C%7Cf53da5b01c8d40301f8b08db9ff46a60%7C84df9e7fe9f640afb435aaaaaaaaaaaa%7C1%7C0%7C638279644331040238%7CUnknown%7CTWFpbGZsb3d8eyJWIjoiMC4wLjAwMDAiLCJQIjoiV2luMzIiLCJBTiI6Ik1haWwiLCJXVCI6Mn0%3D%7C3000%7C%7C%7C&amp;sdata=n0jj0Qt2bridVwj7wtGlRifKurHKXO5RIrfCEy3PxgM%3D&amp;reserved=0\">https:\/\/www.uptodate.com\/contents\/pathology-of-exocrine-pancreatic-neoplasms.<\/a><\/li>\n\n\n\n<li>Asif Khalid, <a href=\"https:\/\/www.uptodate.com\/contents\/pancreatic-cystic-neoplasms-clinical-manifestations-diagnosis-and-management\/contributors\">Kevin McGrath.<\/a> Pancreatic cystic neoplasms: Clinical manifestations, diagnosis, and management. Uptodate 2022. Disponivel em: https:\/\/www.uptodate.com\/contents\/pancreatic-cystic-neoplasms-clinical-manifestations-diagnosis-and-management<a href=\"https:\/\/na01.safelinks.protection.outlook.com\/?url=https%3A%2F%2Fwww.uptodate.com%2Fcontents%2Fpathology-of-exocrine-pancreatic-neoplasms%2Fcontributors&amp;data=05%7C01%7C%7Cf53da5b01c8d40301f8b08db9ff46a60%7C84df9e7fe9f640afb435aaaaaaaaaaaa%7C1%7C0%7C638279644331040238%7CUnknown%7CTWFpbGZsb3d8eyJWIjoiMC4wLjAwMDAiLCJQIjoiV2luMzIiLCJBTiI6Ik1haWwiLCJXVCI6Mn0%3D%7C3000%7C%7C%7C&amp;sdata=n0jj0Qt2bridVwj7wtGlRifKurHKXO5RIrfCEy3PxgM%3D&amp;reserved=0\">.<\/a><\/li>\n\n\n\n<li>Okasha, H., Abbas, W., Altonbary, A. <em>et al.<\/em> Role of endoscopic ultrasonography in the diagnosis of solid pseudo-papillary neoplasm: Egyptian multi-centric case series and systematic review. <em>Egypt J Intern Med<\/em> <strong>34<\/strong>, 9 (2022). <a href=\"https:\/\/na01.safelinks.protection.outlook.com\/?url=https%3A%2F%2Fdoi.org%2F10.1186%2Fs43162-022-00105-z&amp;data=05%7C01%7C%7Cf53da5b01c8d40301f8b08db9ff46a60%7C84df9e7fe9f640afb435aaaaaaaaaaaa%7C1%7C0%7C638279644331040238%7CUnknown%7CTWFpbGZsb3d8eyJWIjoiMC4wLjAwMDAiLCJQIjoiV2luMzIiLCJBTiI6Ik1haWwiLCJXVCI6Mn0%3D%7C3000%7C%7C%7C&amp;sdata=%2FH6Hb32aaH5FduZOCNiFDVuCUQNMReSZbzE3REz9F0c%3D&amp;reserved=0\">https:\/\/doi.org\/10.1186\/s43162-022-00105-z<\/a><\/li>\n<\/ol>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-como-citar-este-artigo\"><strong>Como citar este artigo<\/strong><\/h2>\n\n\n\n<p class=\"has-very-light-gray-to-cyan-bluish-gray-gradient-background has-background\">Passos HL, Souza CS, Martins BC. Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (Tumor de Frantz). Gastropedia 2024 Vol. 1 Dispon\u00edvel em: https:\/\/gastropedia.pub\/pt\/cirurgia\/hepatopancreatobiliar\/neoplasia-pseudopapilar-solida-do-pancreas-tumor-de-frantz<\/p>\n\n\n\n<p><\/p>\n","protected":false},"excerpt":{"rendered":"<p>A Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (NPSP), conhecida previamente como Tumor de Frantz, \u00e9 um tumor geralmente benigno, por\u00e9m com potencial de malignidade. Estas les\u00f5es s\u00e3o raras, representando menos de&hellip;<\/p>\n","protected":false},"author":5752,"featured_media":7923,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[24,28,397],"tags":[],"ano":[396],"tipo":[121],"volume":[57],"class_list":["post-7921","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-cirurgia","category-hepatopancreatobiliar","category-traducao","ano-396","tipo-assuntos-gerais","volume-volume-i"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.3) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (Tumor de Frantz) - Gastropedia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/gastropedia.pub\/pt\/cirurgia\/hepatopancreatobiliar\/neoplasia-pseudopapilar-solida-do-pancreas-tumor-de-frantz\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (Tumor de Frantz)\" \/>\n<meta property=\"og:description\" content=\"A Neoplasia Pseudopapilar S\u00f3lida do P\u00e2ncreas (NPSP), conhecida previamente como Tumor de Frantz, \u00e9 um tumor geralmente benigno, por\u00e9m com potencial de malignidade. 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