{"id":3880,"date":"2022-12-08T06:23:00","date_gmt":"2022-12-08T09:23:00","guid":{"rendered":"https:\/\/gastropedia.pub\/pt\/?p=3880"},"modified":"2024-07-08T09:44:43","modified_gmt":"2024-07-08T12:44:43","slug":"neoplasias-papiliferas-intraductais-produtoras-de-mucina-ipmn","status":"publish","type":"post","link":"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/neoplasias-papiliferas-intraductais-produtoras-de-mucina-ipmn\/","title":{"rendered":"Neoplasias Papil\u00edferas Intraductais Produtoras de Mucina (IPMN)"},"content":{"rendered":"<div class=\"pdfprnt-buttons pdfprnt-buttons-post pdfprnt-top-right\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/3880?print=pdf\" class=\"pdfprnt-button pdfprnt-button-pdf\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/pdf.png\" alt=\"image_pdf\" title=\"Ver PDF\" \/><\/a><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/3880?print=print\" class=\"pdfprnt-button pdfprnt-button-print\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/print.png\" alt=\"image_print\" title=\"Conte\u00fado de impress\u00e3o\" \/><\/a><\/div>\n<p>Os IPMN s\u00e3o as neoplasias c\u00edsticas pancre\u00e1ticas mais frequentes, e em algumas casu\u00edsticas a preval\u00eancia pode chegar a 25%, com maior incid\u00eancia nos pacientes de faixas et\u00e1rias mais avan\u00e7adas. Na maior parte dos casos o diagn\u00f3stico \u00e9 feito acidentalmente, muitas vezes \u00e9 um achado de imagem, o paciente \u00e9 assintom\u00e1tico.<br>A origem do cisto \u00e9 o pr\u00f3prio ducto pancre\u00e1tico, embora a patog\u00eanese n\u00e3o seja clara at\u00e9 hoje. A principal caracter\u00edstica \u00e9 a produ\u00e7\u00e3o de mucina, uma prote\u00edna densa que se acumula nos ductos, causando ectasia e dilata\u00e7\u00e3o dos mesmos.<\/p>\n\n\n\n<p><\/p>\n\n\n\n<details class=\"wp-block-details has-very-light-gray-to-cyan-bluish-gray-gradient-background has-background is-layout-flow wp-block-details-is-layout-flow\"><summary>Saiba mais sobre les\u00f5es c\u00edsticas do p\u00e2ncreas<\/summary>\n<p><a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/cistoadenoma-seroso-de-pancreas\/\">Cisto adenoma seroso do p\u00e2ncreas<\/a><br><a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/cistoadenoma-mucinoso-mcn\/\">Cisto adenoma mucinoso do p\u00e2ncreas<br><\/a><a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/resumo-da-live-desvendando-as-lesoes-cisticas-do-pancreas\">Resumo da Live: les\u00f5es c\u00edsticas do p\u00e2ncreas<\/a><\/p>\n<\/details>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-classificacao\"><br><strong>Classifica\u00e7\u00e3o<\/strong><\/h2>\n\n\n\n<p>Os IPMNs podem ser classificados como:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>IPMNs de ducto principal: quando a dilata\u00e7\u00e3o e ectasia \u00e9 do pr\u00f3prio ducto de<br>Wirsung, podendo acometer o ducto todo ou apenas um segmento;<\/li>\n\n\n\n<li>IPMNs de ductos secund\u00e1rios: quando as dilata\u00e7\u00f5es acometem os ductos menores<br>do p\u00e2ncreas, podendo ser multifocais em at\u00e9 67% dos casos;<\/li>\n\n\n\n<li>IPMNs mistos: acometem tanto ducto principal quanto os ductos secund\u00e1rios, e se<br>comportam como os IPMNs de ducto principal.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image size-large\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM.jpg\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" width=\"1024\" height=\"679\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-1024x679.jpg\" alt=\"\" class=\"wp-image-3889\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-1024x679.jpg?v=1670451626 1024w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-300x199.jpg?v=1670451626 300w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-768x509.jpg?v=1670451626 768w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-1170x776.jpg?v=1670451626 1170w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-780x516.jpg?v=1670451626 780w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-585x388.jpg?v=1670451626 585w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM-263x175.jpg?v=1670451626 263w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/IPMN-RNM.jpg?v=1670451626 1348w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/a><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-quadro-clinico\"><strong>Quadro Cl\u00ednico<\/strong><\/h2>\n\n\n\n<p>A ampla maioria dos pacientes s\u00e3o assintom\u00e1ticos, especialmente os que t\u00eam apenas dilata\u00e7\u00f5es de ductos secund\u00e1rios. Os sintomas que podem aparecer s\u00e3o: desconforto abdominal, icter\u00edcia e perda de peso. O aparecimento de sintomas,<br>especialmente icter\u00edcia, \u00e9 considerado um sinal de alarme, muito sugestivo de maligniza\u00e7\u00e3o. Os pacientes sintom\u00e1ticos dever\u00e3o ser reavaliados com exame de imagem.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-diagnostico\"><br><strong>Diagn\u00f3stico<\/strong><\/h2>\n\n\n\n<p>O diagn\u00f3stico \u00e9 baseado em altera\u00e7\u00e3o de exames de imagem. Como foi dito anteriormente, muitas vezes o diagn\u00f3stico \u00e9 incidental. Apesar disso, ao encontrarmos uma les\u00e3o suspeita de IPMN, \u00e9 necess\u00e1rio o seguimento deste paciente.<br>Os exames de imagem que auxiliam no diagn\u00f3stico e seguimento s\u00e3o:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Tomografia computadorizada: a tomografia n\u00e3o \u00e9 o melhor exame para avalia\u00e7\u00e3o de les\u00f5es c\u00edsticas pancre\u00e1ticas, por\u00e9m pode ser utilizada para pacientes com contraindica\u00e7\u00e3o \u00e0 Resson\u00e2ncia Magn\u00e9tica. O exame deve ser realizado com administra\u00e7\u00e3o de contraste endovenoso em protocolo com 2 fases: arterial e venosa. Auxilia no diagn\u00f3stico diferencial das dilata\u00e7\u00f5es ductais, como no caso de calcifica\u00e7\u00f5es e tumores pancre\u00e1ticos.<\/li>\n<\/ul>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Resson\u00e2ncia Magn\u00e9tica com Colangio Pancreato-resson\u00e2ncia: talvez seja o melhor<br>exame para avalia\u00e7\u00e3o de IPMNs, pois permite ver a comunica\u00e7\u00e3o ductal, determina<br>o exato segmento que a les\u00e3o se encontra e consegue avaliar sinais de<br>preocupa\u00e7\u00e3o, como componente s\u00f3lido intrac\u00edstico, realce na parede da les\u00e3o e<br>acometimento de ducto principal. A MRCP \u00e9 o exame de escolha para a avalia\u00e7\u00e3o<br>do cisto e avalia\u00e7\u00e3o de sinais preocupantes ou sinais de alarme.<\/li>\n\n\n\n<li>Ecoendoscopia ou Ultrassom endosc\u00f3pico: \u00e9 um exame utilizado quando h\u00e1 d\u00favidas<br>diagn\u00f3sticas (diferencia\u00e7\u00e3o entre les\u00e3o mucinosa e n\u00e3o mucinosa, por exemplo) ou<br>quando h\u00e1 suspeita de transforma\u00e7\u00e3o maligna, visto que permite a pun\u00e7\u00e3o do cisto<br>com an\u00e1lise bioqu\u00edmica (dosagem de amilase, CEA e glicose) al\u00e9m de citologia. As<br>les\u00f5es menores de 1 cm n\u00e3o devem ser puncionadas, pois o risco de j\u00e1 serem<br>malignas \u00e9 muito baixo, al\u00e9m de n\u00e3o conseguir material suficiente para an\u00e1lise<br>bioqu\u00edmica. Para a an\u00e1lise citol\u00f3gica que \u00e9 realizada em bloco, h\u00e1 uma tend\u00eancia a<br>utiliza\u00e7\u00e3o de agulhas de bi\u00f3psia (FNB) ao inv\u00e9s de agulhas finas (FNA), o que<br>parece melhorar a acur\u00e1cia dos diagn\u00f3sticos de displasias.<\/li>\n<\/ul>\n\n\n\n<p>O exame de ultrassom convencional tem baixa acur\u00e1cia para diagn\u00f3stico de les\u00f5es c\u00edsticas pancre\u00e1ticas, embora possa ser usado para seguimento das les\u00f5es j\u00e1 bem estabelecidas.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-criterios-de-gravidade\"><br><strong>Crit\u00e9rios de gravidade<\/strong><\/h2>\n\n\n\n<p>O consenso de Fukuoka, datado de 2012, sugere fatores de alto risco para evolu\u00e7\u00e3o dos IPMNs. <\/p>\n\n\n\n<p><strong><em>Os crit\u00e9rios de alarme s\u00e3o:<\/em><\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Envolvimento de ducto principal com dilata\u00e7\u00e3o &gt; 10 mm<\/li>\n\n\n\n<li>N\u00f3dulo mural &gt; 5 mm com capta\u00e7\u00e3o de contraste<\/li>\n\n\n\n<li>Icter\u00edcia obstrutiva<br><\/li>\n<\/ul>\n\n\n\n<p><strong><em>Os chamados sinais \u00a8preocupantes\u00a8 s\u00e3o:<\/em><\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Pancreatite aguda<\/li>\n\n\n\n<li>Cisto &gt; 3cm<\/li>\n\n\n\n<li>Espessamento e hipercapta\u00e7\u00e3o na parede do cisto<\/li>\n\n\n\n<li>Envolvimento do ducto pancre\u00e1tico principal entre 5-9mm<\/li>\n\n\n\n<li>N\u00f3dulo mural sem realce pelo contraste<\/li>\n\n\n\n<li>Transi\u00e7\u00e3o abrupta de calibre do ducto principal, com atrofia do par\u00eanquima distal<\/li>\n\n\n\n<li>Crescimento do cisto &gt; 5 mm em 2 anos<\/li>\n<\/ul>\n\n\n\n<p><\/p>\n\n\n\n<p class=\"has-very-light-gray-to-cyan-bluish-gray-gradient-background has-background\"><strong>Nota:<\/strong> em 2023 houve a publica\u00e7\u00e3o do Guideline de Kyoto com atualiza\u00e7\u00f5es nesses conceitos. Para saber mais confira esses artigos: <a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/guideline-de-kyoto-atualizacoes-na-abordagem-dos-ipmns-parte-i\/\" target=\"_blank\" rel=\"noreferrer noopener\">Guideline de Kyoto &#8211; atualiza\u00e7\u00f5es na abordagem dos IPMNs &#8211; Parte I<\/a>; <a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/guideline-de-kyoto-atualizacoes-na-abordagem-dos-ipmns-parte-ii\/\">Guideline de Kyoto &#8211; atualiza\u00e7\u00f5es na abordagem dos IPMNs &#8211; Parte I<\/a><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-conducao\"><strong>Condu\u00e7\u00e3o<\/strong><\/h2>\n\n\n\n<p>Os pacientes com crit\u00e9rios de alarme dever\u00e3o ser considerados para a cirurgia, caso tenham condi\u00e7\u00f5es para tal procedimento.<br>Os pacientes com \u00a8sinais preocupantes\u00a8devem ser seguidos, e possivelmente puncionados por Ecoendoscopia. Dever\u00e3o ser seguidos conforme o algoritmo de manejo de pacientes com IPMN (figura 1).<br>Os consensos para manejo dos IPMNs est\u00e3o em constante mudan\u00e7a, estabelecendo novos crit\u00e9rios para indica\u00e7\u00e3o de ressec\u00e7\u00e3o cir\u00fargica.<br><\/p>\n\n\n\n<figure class=\"wp-block-image size-full\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka.png\" data-rel=\"penci-gallery-image-content\" ><img decoding=\"async\" width=\"960\" height=\"824\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka.png\" alt=\"\" class=\"wp-image-3890\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka.png 960w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka-300x258.png 300w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka-768x659.png 768w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/12\/Fukuoka-585x502.png 585w\" sizes=\"(max-width: 960px) 100vw, 960px\" \/><\/a><figcaption class=\"wp-element-caption\">Algoritmo para o gerenciamento de suspeita de BD-IPMN. *A pancreatite pode ser uma indica\u00e7\u00e3o cir\u00fargica para al\u00edvio dos sintomas. &amp;. O diagn\u00f3stico diferencial inclui mucina. A mucina pode se mover com a mudan\u00e7a na posi\u00e7\u00e3o do paciente, pode ser deslocada com a lavagem do cisto e n\u00e3o tem fluxo Doppler. As caracter\u00edsticas do n\u00f3dulo tumoral verdadeiro incluem falta de mobilidade, presen\u00e7a de fluxo Doppler e PAAF do n\u00f3dulo mostrando tecido tumoral. @. A presen\u00e7a de paredes espessadas, mucina intraductal ou n\u00f3dulos murais \u00e9 sugestiva de envolvimento do ducto principal. Na sua aus\u00eancia, o envolvimento do ducto principal \u00e9 inconclusivo. Abreviaturas: BD-IPMN, neoplasia mucinosa papilar intraductal do ducto secund\u00e1rio; PAAF, aspira\u00e7\u00e3o por agulha fina.<\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-como-citar-esse-artigo\">Como citar esse artigo<\/h2>\n\n\n\n<p class=\"has-background\" style=\"background-color:#abb7c282\"><em>Marzinotto M. Neoplasias Papil\u00edferas Intraductais Produtoras de Mucina. Gastropedia, 2022. D\u00edsponivel em:<\/em> <a href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/neoplasias-papiliferas-intraductais-produtoras-de-mucina-ipmn\/\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/neoplasias-papiliferas-intraductais-produtoras-de-mucina-ipmn\/<\/a><\/p>\n\n\n\n<p><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-bibliografia\"><strong>Bibliografia<\/strong><\/h2>\n\n\n\n<ol class=\"wp-block-list\">\n<li>Tanaka, M. et al. International consensus guidelines 2012 for the management of IPMN and MCN of the pancreas Pancreatology 12 (2012) 183e197<\/li>\n\n\n\n<li>van Huijgevoort, NCM et al. Diagnosis and management of pancreatic cystic neoplasms: current evidence and guidelines. Nature Reviews | Gastroenterology &amp; Hepatology, 2019.<\/li>\n\n\n\n<li>Sakorafas, GH et al. Primary pancreatic cystic neoplasms revisited. Part III. Intraductal papillary mucinous neoplasms. Surgical Oncology 20 (2011) e109ee118<\/li>\n\n\n\n<li>Elta, GH et al. ACG Clinical Guideline: Diagnosis and Management of Pancreatic Cysts. Am J Gastroenterol 2018; 113:464\u2013479<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>Os IPMN s\u00e3o as neoplasias c\u00edsticas pancre\u00e1ticas mais frequentes, e em algumas casu\u00edsticas a preval\u00eancia pode chegar a 25%, com maior incid\u00eancia nos pacientes de faixas et\u00e1rias mais avan\u00e7adas. Na&hellip;<\/p>\n","protected":false},"author":3341,"featured_media":3889,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[18,23],"tags":[],"ano":[43],"tipo":[],"volume":[44],"class_list":["post-3880","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-gastroenterologia","category-pancreas","ano-43","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.3) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Neoplasias Papil\u00edferas Intraductais Produtoras de Mucina (IPMN) - Gastropedia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/neoplasias-papiliferas-intraductais-produtoras-de-mucina-ipmn\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Neoplasias Papil\u00edferas Intraductais Produtoras de Mucina (IPMN)\" \/>\n<meta property=\"og:description\" content=\"Os IPMN s\u00e3o as neoplasias c\u00edsticas pancre\u00e1ticas mais frequentes, e em algumas casu\u00edsticas a preval\u00eancia pode chegar a 25%, com maior incid\u00eancia nos pacientes de faixas et\u00e1rias mais avan\u00e7adas. 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