{"id":3166,"date":"2022-12-01T06:00:00","date_gmt":"2022-12-01T09:00:00","guid":{"rendered":"https:\/\/gastropedia.pub\/pt\/?p=3166"},"modified":"2022-12-08T13:02:12","modified_gmt":"2022-12-08T16:02:12","slug":"cistoadenoma-mucinoso-mcn","status":"publish","type":"post","link":"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/cistoadenoma-mucinoso-mcn\/","title":{"rendered":"Cistoadenoma Mucinoso (MCN)"},"content":{"rendered":"<div class=\"pdfprnt-buttons pdfprnt-buttons-post pdfprnt-top-right\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/3166?print=pdf\" class=\"pdfprnt-button pdfprnt-button-pdf\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/pdf.png\" alt=\"image_pdf\" title=\"Ver PDF\" \/><\/a><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/3166?print=print\" class=\"pdfprnt-button pdfprnt-button-print\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/print.png\" alt=\"image_print\" title=\"Conte\u00fado de impress\u00e3o\" \/><\/a><\/div>\n<p>O cistoadenoma mucinoso (MCN) \u00e9 uma les\u00e3o c\u00edstica, produtora de mucina, quase que exclusivamente encontrada em mulheres, em uma propor\u00e7\u00e3o de 20:1. O pico de incid\u00eancia \u00e9 na 5a d\u00e9cada de vida.&nbsp;<\/p>\n\n\n\n<p>O cisto tem localiza\u00e7\u00e3o preferencial no corpo e cauda de p\u00e2ncreas. A principal caracter\u00edstica, al\u00e9m do conte\u00fado espesso, rico em mucina, \u00e9 o estroma ovariano encontrado na les\u00e3o, com receptores para estrog\u00eanios e progest\u00e1genos. Na presen\u00e7a de horm\u00f4nios femininos, a les\u00e3o tende a crescer em tamanho. Al\u00e9m disso, \u00e9 uma les\u00e3o que n\u00e3o tem comunica\u00e7\u00e3o com o ducto pancre\u00e1tico, as diferenciando dos IPMNs.&nbsp;<\/p>\n\n\n\n<p>O epit\u00e9lio do cisto \u00e9 composto por c\u00e9lulas colunares, produtoras de mucina. H\u00e1 um risco de transforma\u00e7\u00e3o maligna que varia nos estudos de 0-34%, entretanto ainda n\u00e3o existem marcadores fi\u00e9is que predizem o risco da les\u00e3o malignizar. O que existe s\u00e3o caracter\u00edsticas de imagem que podem sinalizar transforma\u00e7\u00e3o maligna:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>les\u00f5es &gt; 3 cm<\/li>\n\n\n\n<li>presen\u00e7a de n\u00f3dulos murais<\/li>\n\n\n\n<li>dilata\u00e7\u00e3o do ducto pancre\u00e1tico principal (&gt; 6mm)<\/li>\n\n\n\n<li>calcifica\u00e7\u00f5es perif\u00e9ricas<\/li>\n<\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Diagn\u00f3stico<\/strong><\/h2>\n\n\n\n<p>O diagn\u00f3stico dos MCN pode ser dado com um bom exame de imagem, como uma tomografia ou resson\u00e2ncia magn\u00e9tica. Entretanto, caso haja d\u00favida diagn\u00f3stica, h\u00e1 a possibilidade da pun\u00e7\u00e3o por agulha fina (PAAF) via Ecoendoscopia. Nesse caso \u00e9 importante solicitar marcadores bioqu\u00edmicos como: <strong>amilase<\/strong> (tende a ser baixa), <strong>CEA<\/strong> (nas les\u00f5es mucinosas o CEA \u00e9 geralmente &gt; 190 ng\/ml, com uma acur\u00e1cia de 79%) e a <strong>glicose<\/strong> (geralmente baixa em cistos mucinosos &lt; 66 mg\/dl). Quando combinados, a dosagem de CEA e glicose intracisto tem uma acur\u00e1cia de 93% para diagn\u00f3stico de&nbsp; les\u00f5es mucinosas.&nbsp;<\/p>\n\n\n\n<p>Na d\u00favida de transforma\u00e7\u00e3o maligna, solicita-se a citologia do cisto, muito embora a sensibilidade seja baixa para avalia\u00e7\u00e3o de displasia (cerca de 58%), embora a especificidade seja de 96%.&nbsp;<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-full\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/11\/image.png\" data-rel=\"penci-gallery-image-content\" ><img fetchpriority=\"high\" decoding=\"async\" width=\"555\" height=\"278\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/11\/image.png\" alt=\"\" class=\"wp-image-3167\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/11\/image.png 555w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2022\/11\/image-300x150.png 300w\" sizes=\"(max-width: 555px) 100vw, 555px\" \/><\/a><figcaption class=\"wp-element-caption\"><em>Figuras 1 e 2: cistoadenoma mucinoso de cauda pancre\u00e1tica. Fonte: arquivo pessoal<\/em><\/figcaption><\/figure>\n<\/div>\n\n\n<h2 class=\"wp-block-heading\"><strong>Tratamento<\/strong><\/h2>\n\n\n\n<p>Os MCN que n\u00e3o tiverem estigmas de alto risco para maligniza\u00e7\u00e3o pode ser seguidos com exames de imagem (no primeiro ano, um exame a cada 6 meses, e ap\u00f3s esse per\u00edodo, um exame anual), muito embora n\u00e3o haja como excluir a possibilidade de neoplasia sem a ressec\u00e7\u00e3o cir\u00fargica.&nbsp;<\/p>\n\n\n\n<p>Ao optar por realizar o seguimento com imagens, podemos atrasar o tratamento de&nbsp; uma les\u00e3o ressec\u00e1vel. Portanto, essa decis\u00e3o deve levar em considera\u00e7\u00e3o o risco do paciente evoluir com malignidade pancre\u00e1tica, assim como sua idade, expectativa de vida e outros fatores de risco, como obesidade e tabagismo. Al\u00e9m disso, um outro sinal de alarme \u00e9 o diabetes de in\u00edcio recente.&nbsp;<\/p>\n\n\n\n<p>Como os MCN s\u00e3o les\u00f5es que acometem corpo e cauda de p\u00e2ncreas (preferencialmente) a ressec\u00e7\u00e3o dessa por\u00e7\u00e3o pancre\u00e1tica tende a ser menos m\u00f3rbida ao paciente. Al\u00e9m disso, \u00e9 poss\u00edvel realizar a enuclea\u00e7\u00e3o da les\u00e3o, sem obrigatoriedade&nbsp; de pancreatectomia necessariamente.&nbsp;<\/p>\n\n\n\n<p>Ainda como alternativas terap\u00eauticas temos a abla\u00e7\u00e3o da les\u00e3o com etanol ou paclitaxel, ou ainda a abla\u00e7\u00e3o por radiofrequ\u00eancia. Esses procedimentos, entretanto, tem muitos efeitos adversos, e s\u00e3o propostos para pacientes n\u00e3o candidatos a cirurgia. Mais estudos s\u00e3o necess\u00e1rios para indica\u00e7\u00e3o da abla\u00e7\u00e3o como procedimento de rotina.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Progn\u00f3stico<\/strong><\/h2>\n\n\n\n<p>O progn\u00f3stico do paciente que teve o MCN ressecado antes da transforma\u00e7\u00e3o maligna \u00e9 muito bom, com sobrevida em torno de 100% de em 5 anos. J\u00e1 os pacientes operados com MCN invasivos, t\u00eam cerca de 60% de sobrevida em 5 anos. As les\u00f5es &lt; 4 cm sem estigmas de alto risco, tem taxas de maligniza\u00e7\u00e3o de &lt; 0,05%<\/p>\n\n\n\n<p><\/p>\n\n\n\n<pre class=\"wp-block-verse\">Veja tamb\u00e9m nosso artigo sobre Cistoadenoma Seroso de P\u00e2ncreas clicando <a href=\"https:\/\/gastropedia\/gastroenterologia\/pancreas\/cistoadenoma-seroso-de-pancreas\/\" target=\"_blank\" rel=\"noreferrer noopener\">nesse link<\/a><\/pre>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Bibliografia<\/strong><\/h2>\n\n\n\n<ol class=\"wp-block-list\">\n<li>Lopes CV. Cyst fluid glucose: An alternative to carcinoembryonic antigen for &nbsp;pancreatic mucinous cysts. World J Gastroenterol 2019 May 21; 25(19): 2271-2278<\/li>\n\n\n\n<li>Nilsson, LN et al. Nature and management of pancreatic mucinous cystic neoplasm (MCN): A systematic review of the literature. Pancreatology 2016. 1-9.&nbsp;<\/li>\n\n\n\n<li>Elta, GH et al. ACG Clinical Guideline: Diagnosis and Management of Pancreatic Cysts. Am J Gastroenterol 2018; 113:464\u20134<\/li>\n\n\n\n<li>The European Study Group on Cystic Tumours of the Pancreas. European evidence-based guidelines on pancreatic cystic neoplasms. Gut 2018;67:789\u2013804<\/li>\n<\/ol>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Como citar este arquivo<\/strong><\/h2>\n\n\n\n<p class=\"has-background\" style=\"background-color:#abb7c282\"><em>Marzinotto M., CISTOADENOMA MUCINOSO (MCN). Gastropedia, 2022. D\u00edsponivel em:<\/em> <a href=\"https:\/\/gastropedia.pub\/pt\/?p=3166\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/gastropedia\/gastroenterologia\/pancreas\/cistoadenoma-mucinoso-mcn<\/a><\/p>\n\n\n\n<p><\/p>\n","protected":false},"excerpt":{"rendered":"<p>O cistoadenoma mucinoso (MCN) \u00e9 uma les\u00e3o c\u00edstica, produtora de mucina, quase que exclusivamente encontrada em mulheres, em uma propor\u00e7\u00e3o de 20:1. O pico de incid\u00eancia \u00e9 na 5a d\u00e9cada&hellip;<\/p>\n","protected":false},"author":3341,"featured_media":3168,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[18,23],"tags":[133,132],"ano":[43],"tipo":[],"volume":[44],"class_list":["post-3166","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-gastroenterologia","category-pancreas","tag-cistoadenoma","tag-cistoadenoma-mucinoso","ano-43","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.3) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Cistoadenoma Mucinoso (MCN) - Gastropedia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/pancreas\/cistoadenoma-mucinoso-mcn\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cistoadenoma Mucinoso (MCN)\" \/>\n<meta property=\"og:description\" content=\"O cistoadenoma mucinoso (MCN) \u00e9 uma les\u00e3o c\u00edstica, produtora de mucina, quase que exclusivamente encontrada em mulheres, em uma propor\u00e7\u00e3o de 20:1. 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