{"id":10063,"date":"2025-07-10T06:30:00","date_gmt":"2025-07-10T09:30:00","guid":{"rendered":"https:\/\/gastropedia.pub\/pt\/?p=10063"},"modified":"2025-07-09T22:58:38","modified_gmt":"2025-07-10T01:58:38","slug":"fire-uma-sindrome-emergente-associada-a-esofagite-eosinofilica","status":"publish","type":"post","link":"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/fire-uma-sindrome-emergente-associada-a-esofagite-eosinofilica\/","title":{"rendered":"FIRE: Uma S\u00edndrome Emergente Associada \u00e0 Esofagite Eosinof\u00edlica"},"content":{"rendered":"<div class=\"pdfprnt-buttons pdfprnt-buttons-post pdfprnt-top-right\"><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/10063?print=pdf\" class=\"pdfprnt-button pdfprnt-button-pdf\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/pdf.png\" alt=\"image_pdf\" title=\"Ver PDF\" \/><\/a><a href=\"https:\/\/gastropedia.pub\/pt\/wp-json\/wp\/v2\/posts\/10063?print=print\" class=\"pdfprnt-button pdfprnt-button-print\" target=\"_blank\" ><img decoding=\"async\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/plugins\/pdf-print\/images\/print.png\" alt=\"image_print\" title=\"Conte\u00fado de impress\u00e3o\" \/><\/a><\/div>\n<p>A <strong>esofagite eosinof\u00edlica (EoE)<\/strong> \u00e9 uma condi\u00e7\u00e3o esof\u00e1gica cr\u00f4nica, de origem imunol\u00f3gica, associada \u00e0 inflama\u00e7\u00e3o do tipo 2 e caracterizada por eosinofilia esof\u00e1gica. Frequentemente, est\u00e1 associada a outras condi\u00e7\u00f5es at\u00f3picas do tipo 2, como dermatite at\u00f3pica, alergia alimentar mediada por IgE e rinite al\u00e9rgica.<\/p>\n\n\n\n<p>A EoE \u00e9 caracterizada por sintomas de disfun\u00e7\u00e3o motora esof\u00e1gica associados \u00e0 infiltra\u00e7\u00e3o eosinof\u00edlica da mucosa esof\u00e1gica em resposta a al\u00e9rgenos alimentares e\/ou ambientais. O diagn\u00f3stico consiste na contagem de <strong>mais de 15 eosin\u00f3filos por campo de grande aumento <\/strong>em bi\u00f3psias esof\u00e1gicas, ap\u00f3s a exclus\u00e3o de outras causas comuns de eosinofilia esof\u00e1gica.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-e-o-que-e-a-sindrome-fire\"><br><strong>E o que \u00e9 a s\u00edndrome FIRE?<\/strong><\/h2>\n\n\n\n<p>A<strong> S\u00edndrome FIRE (Food-Induced Immediate Response of the Esophagus)<\/strong>, por sua vez, \u00e9 uma nova entidade cl\u00ednica observada em pacientes com <strong>esofagite eosinof\u00edlica (EoE)<\/strong>, caracterizada por uma <strong>resposta de hipersensibilidade imediata<\/strong> ap\u00f3s o consumo de certos alimentos ou bebidas, com<strong> sintomas agudos e reprodut\u00edveis.<\/strong><\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-fisiopatologia\">Fisiopatologia<\/h2>\n\n\n\n<p>Embora ainda n\u00e3o completamente elucidada, discute-se algumas possibilidade, tais como:\u00a0<\/p>\n\n\n\n<div class=\"wp-block-group\"><div class=\"wp-block-group__inner-container is-layout-constrained wp-block-group-is-layout-constrained\">\n<ul class=\"wp-block-list\">\n<li><strong>Hipersensibilidade local mediada por IgE<\/strong>.<\/li>\n\n\n\n<li><strong>Ativa\u00e7\u00e3o de mast\u00f3citos<\/strong> na mucosa e camada muscular esof\u00e1gica.<\/li>\n\n\n\n<li><strong>Barreira epitelial comprometida<\/strong> facilitando a entrada de al\u00e9rgenos.<\/li>\n\n\n\n<li><strong>Intera\u00e7\u00e3o neuroimune<\/strong> (via canais TRPV1\/ASICs) gerando hipersensibilidade sensorial.<\/li>\n<\/ul>\n<\/div><\/div>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-caracteristicas-clinicas\">Caracter\u00edsticas cl\u00ednicas<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Sintomas principais:<\/strong> dor retroesternal, sensa\u00e7\u00e3o de aperto, queima\u00e7\u00e3o, sufocamento ou ansiedade logo ap\u00f3s a ingest\u00e3o dos alimentos.<\/li>\n\n\n\n<li><strong>In\u00edcio<\/strong>: geralmente ocorre <strong>em at\u00e9 5 minutos<\/strong> ap\u00f3s o contato com o gatilho.<\/li>\n\n\n\n<li><strong>Dura\u00e7\u00e3o<\/strong>: entre minutos at\u00e9 2 horas; na maioria, menos de 30 minutos.<\/li>\n\n\n\n<li><strong>Intensidade<\/strong>: elevada (\u22657 em escala anal\u00f3gica visual).<\/li>\n\n\n\n<li><strong>Gatilhos comuns<\/strong>: frutas, vegetais, latic\u00ednios, vinho, cerveja, vinagre.<\/li>\n<\/ul>\n\n\n\n<p>Curiosamente, os <strong>principais alimentos gatilho n\u00e3o coincidem com alguns dos principais desencadeadores da EoE (trigo, ovo e soja)<\/strong>, o que sugere que os mecanismos de FIRE podem ser distintos \u2013 ou at\u00e9 sobrepostos \u2013 aos da inflama\u00e7\u00e3o eosinof\u00edlica tradicional.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-fire-e-diferente-da-disfagia-classica-da-eoe-e-da-sindrome-da-alergia-oral\"><strong>FIRE \u00e9 diferente da disfagia cl\u00e1ssica da EoE e da s\u00edndrome da alergia oral<\/strong><\/h2>\n\n\n\n<p>Embora alguns sintomas possam lembrar a<strong> s\u00edndrome de alergia oral (SAO)<\/strong>, o FIRE \u00e9 distinto: <strong>a rea\u00e7\u00e3o se localiza no es\u00f4fago e n\u00e3o na orofaringe<\/strong>. Al\u00e9m disso, os pacientes reconhecem claramente a diferen\u00e7a entre FIRE e epis\u00f3dios de disfagia ou impacta\u00e7\u00e3o alimentar comuns na EoE.<\/p>\n\n\n\n<figure class=\"wp-block-table is-style-stripes has-normal-font-size\"><div class=\"pcrstb-wrap\"><table class=\"has-very-light-gray-to-cyan-bluish-gray-gradient-background has-background has-fixed-layout\"><thead><tr><th><strong>Caracter\u00edstica<\/strong><\/th><th><strong>FIRE<\/strong><\/th><th><strong>EoE cl\u00e1ssica<\/strong><\/th><th><strong>SAO<\/strong><\/th><\/tr><\/thead><tbody><tr><td><strong>In\u00edcio ap\u00f3s alimenta\u00e7\u00e3o<\/strong><br><\/td><td>Imediato (&lt;5min)<br><\/td><td>Vari\u00e1vel (disfagia tardia)<\/td><td>Imediato (&lt;5min)<\/td><\/tr><tr><td><strong>Dura\u00e7\u00e3o dos sintomas<\/strong><\/td><td>Minutos at\u00e9 2h<\/td><td>Prolongado, cr\u00f4nico<\/td><td>Minutos<\/td><\/tr><tr><td><strong>Localiza\u00e7\u00e3o<\/strong><\/td><td>Esof\u00e1gica (retroesternal)<\/td><td>Esof\u00e1gica<\/td><td>Orofaringe (l\u00e1bios, l\u00edngua e palato)<\/td><\/tr><tr><td><br><strong>Sintomas principais<\/strong><\/td><td>Queima\u00e7\u00e3o, estreitamento, engasgo, ansiedade<\/td><td>Disfagia, impacta\u00e7\u00e3o<\/td><td>Prurido oral, formigamento<\/td><\/tr><tr><td><strong>Desencadeantes comuns<\/strong><\/td><td>Frutas, vinho, latic\u00ednios e nozes<\/td><td>Leite, trigo, ovo e soja<\/td><td>Frutas e vegetais frescos<\/td><\/tr><tr><td><strong>Associa\u00e7\u00e3o com atopias<\/strong><\/td><td>Frequente<\/td><td>Frequente<\/td><td>Muito frequente<\/td><\/tr><tr><td><strong>Endoscopia e bi\u00f3psia<\/strong><\/td><td>Pode ser normal<\/td><td>Eosinofilia esof\u00e1gica (&gt;15 eos\/CGA)<\/td><td>Normal<\/td><\/tr><\/tbody><\/table><\/div><figcaption class=\"wp-element-caption\"><br><em>Tabela 1. Principais diferen\u00e7as entre FIRE (Food-induced Immediate Response of the Esophagus, SAO (s\u00edndroma da alergia oral) e EoE (Esofagite eosinof\u00edlica)<\/em><\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-epidemiologia-e-diagnostico\">Epidemiologia e diagn\u00f3stico<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li>At\u00e9 40% dos pacientes com EoE podem apresentar quadros sugestivos de s\u00edndrome FIRE<\/li>\n\n\n\n<li><strong>FIRE pode preceder ou ocorrer independentemente da atividade da EoE.<\/strong><\/li>\n\n\n\n<li>Ainda <strong>n\u00e3o h\u00e1 crit\u00e9rios diagn\u00f3sticos padronizados<\/strong>; o diagn\u00f3stico \u00e9 <strong>cl\u00ednico e baseado na reprodutibilidade dos sintomas<\/strong>.<\/li>\n<\/ul>\n\n\n\n<figure class=\"wp-block-image size-full\"><a href=\"https:\/\/gastropedia.pub\/pt\/?attachment_id=10064\"><img fetchpriority=\"high\" decoding=\"async\" width=\"684\" height=\"530\" src=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2025\/06\/Algoritmo-de-avaliacao-de-sintomas-esofagicos-pos-alimentares.png\" alt=\"\" class=\"wp-image-10064\" srcset=\"https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2025\/06\/Algoritmo-de-avaliacao-de-sintomas-esofagicos-pos-alimentares.png 684w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2025\/06\/Algoritmo-de-avaliacao-de-sintomas-esofagicos-pos-alimentares-300x232.png 300w, https:\/\/gastropedia.pub\/pt\/wp-content\/uploads\/2025\/06\/Algoritmo-de-avaliacao-de-sintomas-esofagicos-pos-alimentares-585x453.png 585w\" sizes=\"(max-width: 684px) 100vw, 684px\" \/><\/a><figcaption class=\"wp-element-caption\"><br><em>Algoritmo de avalia\u00e7\u00e3o de sintomas esof\u00e1gicos p\u00f3s alimentares<\/em><\/figcaption><\/figure>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-conclusao\"><strong>Conclus\u00e3o<\/strong><\/h2>\n\n\n\n<p>A s\u00edndrome FIRE representa uma <strong>nova dimens\u00e3o dos sintomas esof\u00e1gicos em pacientes com EoE<\/strong>, exigindo aten\u00e7\u00e3o especial dos profissionais de sa\u00fade, especialmente gastroenterologistas, alergistas e nutricionistas. Compreender esse fen\u00f4meno pode melhorar o cuidado cl\u00ednico, otimizar estrat\u00e9gias de elimina\u00e7\u00e3o alimentar e, quem sabe, lan\u00e7ar luz sobre os mecanismos imunes da EoE.<\/p>\n\n\n\n<p>Mais estudos s\u00e3o necess\u00e1rios para estabelecer crit\u00e9rios diagn\u00f3sticos, entender sua fisiopatologia e desenvolver tratamentos eficazes.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-referencias\"><br><strong>Refer\u00eancias<\/strong><\/h2>\n\n\n\n<ol class=\"wp-block-list\">\n<li>Koken G, Ertoy Karagol H, Polat Terece S, et al.\u00a0Food-induced immediate response of the esophagus (FIRE) in pediatric eosinophilic esophagitis.\u00a0<em>Authorea<\/em>. 2023 Jun 8. doi:<a href=\"https:\/\/doi.org\/10.22541\/au.168620695.51164151\/v1\">10.22541\/au.168620695.51164151\/v1<\/a>.<\/li>\n\n\n\n<li>Ali S, Cernat MC, Vintil\u0103 MR, Berghea EC, Bumb\u0103cea RS. Shedding Light on FIRE Syndrome: An Overview of a Novel Condition in Eosinophilic Esophagitis.\u00a0<em>Applied Sciences<\/em>. 2025; 15(11):6375. <a href=\"https:\/\/doi.org\/10.3390\/app15116375\">https:\/\/doi.org\/10.3390\/app15116375<\/a><\/li>\n\n\n\n<li>Biedermann L, Holbreich M, Atkins D, Chehade M, Dellon ES, Furuta GT, Hirano I, Gonsalves N, Greuter T, Gupta S, Katzka DA, De Rooij W, Safroneeva E, Schoepfer A, Schreiner P, Simon D, Simon HU, Warners M, Bredenoord AJ, Straumann A. Food-induced immediate response of the esophagus-A newly identified syndrome in patients with eosinophilic esophagitis. <em>Allergy<\/em>. 2021 Jan;76(1):339-347. <a href=\"https:\/\/doi.org\/10.1111\/all.14495\">doi: 10.1111\/all.14495<\/a>.<\/li>\n<\/ol>\n\n\n\n<h2 class=\"wp-block-heading\" id=\"h-como-citar-este-artigo\"><strong>Como citar este artigo<\/strong><\/h2>\n\n\n\n<p class=\"has-very-light-gray-to-cyan-bluish-gray-gradient-background has-background\">Nobre K. FIRE: Uma S\u00edndrome Emergente Associada \u00e0 Esofagite Eosinof\u00edlica Gastropedia 2025, Vol II. Dispon\u00edvel em: <a href=\"https:\/\/gastropedia.pub\/pt\/?p=10063\" target=\"_blank\" rel=\"noreferrer noopener\">https:\/\/gastropedia.pub\/pt\/gastroenterologia\/fire-uma-sindrome-emergente-associada-a-esofagite-eosinofilica\/<\/a><\/p>\n\n\n\n<p><\/p>\n","protected":false},"excerpt":{"rendered":"<p>A esofagite eosinof\u00edlica (EoE) \u00e9 uma condi\u00e7\u00e3o esof\u00e1gica cr\u00f4nica, de origem imunol\u00f3gica, associada \u00e0 inflama\u00e7\u00e3o do tipo 2 e caracterizada por eosinofilia esof\u00e1gica. Frequentemente, est\u00e1 associada a outras condi\u00e7\u00f5es at\u00f3picas&hellip;<\/p>\n","protected":false},"author":5852,"featured_media":10093,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"","_lmt_disable":"","footnotes":""},"categories":[19,18],"tags":[],"ano":[413],"tipo":[121],"volume":[44],"class_list":["post-10063","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-esofago","category-gastroenterologia","ano-413","tipo-assuntos-gerais","volume-volume-ii"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v27.2 (Yoast SEO v27.3) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>FIRE: Uma S\u00edndrome Emergente Associada \u00e0 Esofagite Eosinof\u00edlica - Gastropedia<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/gastropedia.pub\/pt\/gastroenterologia\/fire-uma-sindrome-emergente-associada-a-esofagite-eosinofilica\/\" \/>\n<meta property=\"og:locale\" content=\"pt_BR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"FIRE: Uma S\u00edndrome Emergente Associada \u00e0 Esofagite Eosinof\u00edlica\" \/>\n<meta property=\"og:description\" content=\"A esofagite eosinof\u00edlica (EoE) \u00e9 uma condi\u00e7\u00e3o esof\u00e1gica cr\u00f4nica, de origem imunol\u00f3gica, associada \u00e0 inflama\u00e7\u00e3o do tipo 2 e caracterizada por eosinofilia esof\u00e1gica. 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